Urine Odour

Sweet or fruity odourKetoacidosis (Diabetic, alcoholic, starvation)
Maple syrup urine disease (infants, rare)
Ammoniacal odourBladder retention
Urine at room temperature for prolonged period (“alkaline fermentaion”)
Bacterial infection
Faecal odourBladder-Intestinal fistula
E. coli infection
Contamination with feces
Musty odourPhenylketonuria
Sulfur odourCysteine decomposition
Suppurative diseases of the GU tract
Faintly AromaticVolatile organic acids most marked in “concentrated” urine specimens
Swimming pool odourHawkinsinuria
Mousy odour
Cabbage-like odour
Tyrosinemia
Drugs and dietCharacteristic odour of many drugs such as antibiotics (e.g. penicillins); food (e.g. asparagus)
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About Mike Cadogan

Emergency physician with a passion for medical informatics and medical education. Co-founder of HealthEngine, iMeducate, and the GMEP. He writes more eclectically on the web as @sandnsurf | + Mike Cadogan | Contact